Difference between revisions of "Template:Inborn errors of carbohydrate metabolism"

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{{Navbox
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| name  = Inborn errors of carbohydrate metabolism
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| title = [[Inborn error of metabolism|Inborn error]] of [[Inborn errors of carbohydrate metabolism|carbohydrate metabolism]]: [[monosaccharide]] metabolism disorders (including [[glycogen storage disease]]s) ([[ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases#(E73–E74) Carbohydrates|E73–E74]], [[List of ICD-9 codes 240–279: endocrine, nutritional and metabolic diseases, and immunity disorders#Disorders of carbohydrate transport and metabolism|271]])
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| state = {{{state|autocollapse}}}
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| titlestyle = background:Silver
  
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| group1 = [[Sucrose]], transport<br />(extracellular)
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|  list1 = {{Navbox subgroup
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| group1 = [[Disaccharide]] catabolism
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| list1  = [[Lactose intolerance]]{{·}} [[Sucrose intolerance]]
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| group3 = [[Monosaccharide]] transport
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|  list3 = [[Glucose-galactose malabsorption]]{{·}} [[Inborn errors of renal tubular transport]] ([[Renal glycosuria]]){{·}} [[Fructose malabsorption]]
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}}
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| group3 = [[Hexose]] → [[glucose]]
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|  list3 = {{Navbox subgroup
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| group2 = [[Monosaccharide]] catabolism
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|  list2 = <div>''[[fructose]]'': [[Essential fructosuria]]{{·}} [[Hereditary fructose intolerance|Fructose intolerance]]</div>
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<div>''[[galactose]]/[[galactosemia]] :'' [[Galactokinase deficiency|GALK deficiency]]{{·}} [[Galactose-1-phosphate uridylyltransferase galactosemia|GALT deficiency]]/[[Galactose epimerase deficiency|GALE deficiency]]</div>
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}}
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| group4 = [[Glucose]] ⇄ [[glycogen]]
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|  list4 = {{Navbox subgroup
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| group1 = [[Glycogenesis]]
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| list1  = [[Glycogen storage disease type 0|GSD type 0, glycogen synthase]]{{·}} [[Glycogen storage disease type IV|GSD type IV, Andersen's, branching]]
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| group8 = [[Glycogenolysis]]
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|  list8 = <div>extralysosomal: [[Glycogen storage disease type V|GSD type V, McArdle, muscle glycogen phosphorylase]]/[[Glycogen storage disease type VI|GSD type VI, Hers', liver glycogen phosphorylase]]{{·}} [[Glycogen storage disease type III|GSD type III, Cori's, debranching]]</div>
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<div>[[Lysosome|lysosomal]]/[[Lysosomal storage disease|LSD]]: [[Glycogen storage disease type II|GSD type II, Pompe's, glucosidase]]</div>
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}}
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| group7 = [[Glucose]] ⇄ [[Citric acid cycle|CAC]]
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|  list7 = {{Navbox subgroup
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| group1 = [[Glycolysis]]
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| list1  = [[MODY 2]]/[[Hyperinsulinemic hypoglycemia|HHF3]]{{·}} [[Phosphofructokinase deficiency|GSD type VII, Tarui's, phosphofructokinase]]{{·}} [[Triosephosphate isomerase deficiency]]{{·}} [[Pyruvate kinase deficiency]]
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| group6 = [[Gluconeogenesis]]
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|  list6 = [[Pyruvate carboxylase deficiency|PCD]]{{·}} [[Fructose bisphosphatase deficiency]]{{·}} [[Glycogen storage disease type I|GSD type I, von Gierke, glucose 6-phosphatase]]
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}}
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| group9 = [[Pentose phosphate pathway]]
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|  list9 = [[Glucose-6-phosphate dehydrogenase deficiency]]
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| group10 = Other
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| list10 = [[Hyperoxaluria]] ([[Primary hyperoxaluria]]){{·}} [[Pentosuria]]
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| belowstyle = padding:0px;
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| below = {{Metabolic navs}}
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}}<noinclude>
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[[Category:Inborn errors of carbohydrate metabolism]]
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[[Category:Metabolic disorder templates|{{PAGENAME}}]]
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</noinclude>

Revision as of 09:01, 31 January 2011