| Porphyrin biosynthesis | early mitochondrial: D-Aminolevulinic acid
cytosolic: Porphobilinogen · Hydroxymethylbilane · Uroporphyrinogen III · Coproporphyrinogen III late mitochondrial: Protoporphyrinogen IX · Protoporphyrin IX | ||||||||||||
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| Heme degradation and excretion | |||||||||||||
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